Classifying Heterotaxy Syndrome
نویسندگان
چکیده
منابع مشابه
Heterotaxy Syndrome
Heterotaxy is defined as an abnormality where the internal thoraco-abdominal organs demonstrate abnormal arrangement across the left-right axis of the body. This broad term includes patients with a wide variety of very complex cardiac lesions. Patients with heterotaxy can be stratified into the subsets of asplenia syndrome and polysplenia syndrome, or the subsets of heterotaxy with isomerism of...
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Heterotaxy syndrome is found infrequently in the adult population. The syndrome is characterized by the presence of abnormal position of the viscera. If the patient does not present with cardiac anomalies incompatible with life, it can be asymptomatic, being diagnosed only incidentally in adulthood (5-10%). We present the case of a 36-year-old with heterotaxy syndrome who was diagnosed after pr...
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Polysplenia/heterotaxy syndrome is a rare congenital disorder associated with a wide spectrum of anomalies in various organ systems. Although anomalies of the cardiovascular system are common in this syndrome, the authors report a rare case of polysplenia syndrome associated with aortic pseudocoarctation, which to our knowledge has never been reported.
متن کاملA Rare Variation of the Heterotaxy Syndrome
Heterotaxy syndrome is a rare, complex, and confusing type of the situs anomalies. It is not possible to estimate the degree of lateralization, isomerism, and rotational variation in these types of cases. Heart and abdominal organ anatomy is specific to the individual, and it should be defined specifically on the basis of each case due to possible cardiac and extracardiac surgical interventions...
متن کاملSimultaneous complex single ventricle palliation and tracheoplasty for heterotaxy syndrome.
Although isomerism of the bronchial tree is an integral part of hetrotaxy syndrome, the association of congenital tracheal stenosis is rare in this group of disorders, and it has not yet been thoroughly described in the literature. This condition is potentially life-threatening and precludes single ventricle palliation. This report presents the case of a 5-month old infant with symptomatic cong...
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ژورنال
عنوان ژورنال: Circulation: Cardiovascular Imaging
سال: 2018
ISSN: 1941-9651,1942-0080
DOI: 10.1161/circimaging.118.007490